Código SKU: E-AB-18489_120μL-ES

Anticuerpo policlonal VCP, 120 μL

La VCP (proteína que contiene valosina) pertenece a la familia de las ATPasas AAA. Se identificó inicialmente como resultado de los intentos de clonar una posible hormona peptídica llamada valosina. Se descubrió que el ADNc clonado codificaba una proteína citosólica de 90 kDa de expresión ubicua, denominada VCP, que no presentaba ninguna de las características de un precursor de hormona peptídica. Los defectos en la VCP son la causa de la miopatía por cuerpos de inclusión con enfermedad de Paget de inicio temprano y demencia frontotemporal (IBMPFD, por sus siglas en inglés) y la esclerosis lateral amiotrófica tipo 14 con o sin demencia frontotemporal (ELA14).

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