Código SKU: PKSH033306_10μg-ES

Proteína GM2A humana recombinante (células humanas, etiqueta His), 10 μg

El activador del gangliósido GM2 (GM2A) es una pequeña proteína transportadora de glucolípidos que actúa como cofactor específico de sustrato para la enzima lisosomal β-hexosaminidasa A (HEXB). HEXB, junto con GM2A, cataliza la degradación del gangliósido GM2 y otras moléculas que contienen N-acetil hexosaminas terminales. GM2A alberga varios fosfolípidos y ácidos grasos monocatenarios y es una proteína de transferencia de lípidos que estimula el procesamiento enzimático de los gangliósidos y la activación de los linfocitos T mediante la presentación lipídica. Extrae moléculas individuales de GM2 de las membranas y las presenta en forma soluble a la β-hexosaminidasa A para la escisión de la N-acetil-D-galactosamina y su conversión a GM3.

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