Código SKU: E-AB-52452_20μL-ES

Anticuerpo policlonal ASS1, 20 μL

La ASS1 es una enzima limitante del ciclo de la urea. La citrulinemia tipo I es un trastorno autosómico recesivo causado por una deficiencia de la enzima argininosuccinato sintetasa (ASS1), que forma parte del ciclo de la urea. La deficiencia de ASS1 presenta diversas manifestaciones clínicas, desde pacientes gravemente afectados con hiperamonemia neonatal mortal hasta individuos asintomáticos con un fenotipo bioquímico únicamente.

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:Porcelana

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Shipping:El producto se envía con una bolsa de hielo. Al recibirlo, guárdelo inmediatamente a la temperatura recomendada.

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Calculated Molecular Weight:47 kDa

Observed Molecular Weight:Consulte las figuras

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Shelf Life:12 meses

Storage:Conservar a -20 °C. Válido durante 12 meses. Evitar ciclos de congelación y descongelación.

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Calculated Molecular Weight:47 kDa

Dilution:WB 1:500-1:2000

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Application:WB

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Research Areas:Cáncer; Metabolismo; Transducción de señales

Species Reactivity:Humano; Ratón; Rata

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Target Synonym:Argininosuccinato sintasa 1; Argininosuccinato sintasa; Argininosuccinato sintetasa 1; ASS; Ass-1; ass1; Assa; Assy; Citrulina aspartato ligasa; Citrulina aspartato ligasa; CTLN1

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Buffer:PBS con 0,05% de NaN3 y 40% de glicerol, pH 7,4

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